20082019

Research output per year

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Article
2019

Mitochondrial dynamics of proximal tubular epithelial cells in nephropathic cystinosis

Rasmo, D. D., Signorile, A., De Leo, E., Polishchuk, E. V., Ferretta, A., Raso, R., Russo, S., Polishchuk, R., Emma, F. & Bellomo, F., 2019, In : International Journal of Molecular Sciences. 21, 1, 192.

Research output: Contribution to journalArticle

Open Access
2018

Impact of atypical mitochondrial cyclic-AMP level in nephropathic cystinosis

Bellomo, F., Signorile, A., Tamma, G., Ranieri, M., Emma, F. & De Rasmo, D., Sep 2018, In : Experientia. 75, 18, p. 3411-3422 12 p.

Research output: Contribution to journalArticle

2017

Inhibition of Drp1-mediated mitochondrial fission improves mitochondrial dynamics and bioenergetics stimulating neurogenesis in hippocampal progenitor cells from a Down syndrome mouse model

Valenti, D., Rossi, L., Marzulli, D., Bellomo, F., De Rasmo, D., Signorile, A. & Vacca, R. A., Dec 1 2017, In : Biochimica et Biophysica Acta - Molecular Basis of Disease. 1863, 12, p. 3117-3127 11 p.

Research output: Contribution to journalArticle

2016

Activation of the transcription factor EB rescues lysosomal abnormalities in cystinotic kidney cells

Rega, L. R., Polishchuk, E., Montefusco, S., Napolitano, G., Tozzi, G., Zhang, J., Bellomo, F., Taranta, A., Pastore, A., Polishchuk, R., Piemonte, F., Medina, D. L., Catz, S. D., Ballabio, A. & Emma, F., Apr 1 2016, In : Kidney International. 89, 4, p. 862-873 12 p.

Research output: Contribution to journalArticle

Carboxyl-Terminal SSLKG Motif of the Human Cystinosin-LKG Plays an Important Role in Plasma Membrane Sorting

Bellomo, F., Taranta, A., Petrini, S., Venditti, R., Rocchetti, M. T., Rega, L. R., Corallini, S., Gesualdo, L., De Matteis, M. A. & Emma, F., 2016, In : PLoS One. 11, 5, p. e0154805

Research output: Contribution to journalArticle

Cystinosin-LKG rescues cystine accumulation and decreases apoptosis rate in cystinotic proximal tubular epithelial cells

Taranta, A., Bellomo, F., Petrini, S., Polishchuk, E. V., De Leo, E., Rega, L. R., Pastore, A., Polishchuk, R. S., De Matteis, M. A. & Emma, F., Sep 22 2016, In : Pediatric Research. 81, 1-1, p. 113-119 7 p.

Research output: Contribution to journalArticle

2015
2014

Gender-related effects on urine l-cystine metastability

Masotti, A., Laurenzi, C., Boenzi, S., Pastore, A., Taranta, A., Bellomo, F., Muraca, M., Dionisi-Vici, C., Bertucci, P., Strologo, L. D. & Emma, F., Feb 2014, In : Amino Acids. 46, 2, p. 415-427 13 p.

Research output: Contribution to journalArticle

2012

Distribution of cystinosin-LKG in human tissues

Taranta, A., Petrini, S., Citti, A., Boldrini, R., Corallini, S., Bellomo, F., Levtchenko, E. & Emma, F., Aug 2012, In : Histochemistry and Cell Biology. 138, 2, p. 351-363 13 p.

Research output: Contribution to journalArticle

Stem cell microvesicles transfer cystinosin to human cystinotic cells and reduce cystine accumulation in vitro

Iglesias, D. M., El-Kares, R., Taranta, A., Bellomo, F., Emma, F., Besouw, M., Levtchenko, E., Toelen, J., van den Heuvel, L., Chu, L., Zhao, J., Young, Y. K., Eliopoulos, N. & Goodyer, P., Aug 13 2012, In : PLoS One. 7, 8, e42840.

Research output: Contribution to journalArticle

2011

Transcriptional and posttranscriptional regulation of the CTNS gene

Corallini, S., Taranta, A., Bellomo, F., Palma, A., Pastore, A. & Emma, F., Aug 2011, In : Pediatric Research. 70, 2, p. 130-135 6 p.

Research output: Contribution to journalArticle

2010

Analysis of CTNS gene transcripts in nephropathic cystinosis

Taranta, A., Wilmer, M. J., Van Den Heuvel, L. P., Bencivenga, P., Bellomo, F., Levtchenko, E. N. & Emma, F., Jul 2010, In : Pediatric Nephrology. 25, 7, p. 1263-1267 5 p.

Research output: Contribution to journalArticle

Modulation of CTNS gene expression by intracellular thiols

Bellomo, F., Corallini, S., Pastore, A., Palma, A., Laurenzi, C., Emma, F. & Taranta, A., Apr 1 2010, In : Free Radical Biology and Medicine. 48, 7, p. 865-872 8 p.

Research output: Contribution to journalArticle

2008

Identification and subcellular localization of a new cystinosin isoform

Taranta, A., Petrini, S., Palma, A., Mannucci, L., Wilmer, M. J., De Luca, V., Diomedi-Camassei, F., Corallini, S., Bellomo, F., Van Den Heuvel, L. P., Levtchenko, E. N. & Emma, F., May 2008, In : American Journal of Physiology - Renal Physiology. 294, 5

Research output: Contribution to journalArticle