A new case of idiopathic hemiplegia hemiconvulsion syndrome

Emilio Franzoni, Caterina Garone, Valentina Marchiani, Daniela Brunetto, Caterina Tonon, Raffaele Lodi, Bruno Bernardi

Research output: Contribution to journalArticle

Abstract

We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.

Original languageEnglish
Pages (from-to)799-805
Number of pages7
JournalNeurological Sciences
Volume31
Issue number6
DOIs
Publication statusPublished - Dec 2010

Keywords

  • Epilepsy
  • Hemiplegia hemiconvulsion
  • MRI
  • Proton MR spectroscopy

ASJC Scopus subject areas

  • Clinical Neurology
  • Psychiatry and Mental health
  • Dermatology

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