Abstract
We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
| Original language | English |
|---|---|
| Pages (from-to) | 799-805 |
| Number of pages | 7 |
| Journal | Neurological Sciences |
| Volume | 31 |
| Issue number | 6 |
| DOIs | |
| Publication status | Published - Dec 2010 |
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Keywords
- Epilepsy
- Hemiplegia hemiconvulsion
- MRI
- Proton MR spectroscopy
ASJC Scopus subject areas
- Clinical Neurology
- Psychiatry and Mental health
- Dermatology
Cite this
A new case of idiopathic hemiplegia hemiconvulsion syndrome. / Franzoni, Emilio; Garone, Caterina; Marchiani, Valentina; Brunetto, Daniela; Tonon, Caterina; Lodi, Raffaele; Bernardi, Bruno.
In: Neurological Sciences, Vol. 31, No. 6, 12.2010, p. 799-805.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - A new case of idiopathic hemiplegia hemiconvulsion syndrome
AU - Franzoni, Emilio
AU - Garone, Caterina
AU - Marchiani, Valentina
AU - Brunetto, Daniela
AU - Tonon, Caterina
AU - Lodi, Raffaele
AU - Bernardi, Bruno
PY - 2010/12
Y1 - 2010/12
N2 - We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
AB - We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
KW - Epilepsy
KW - Hemiplegia hemiconvulsion
KW - MRI
KW - Proton MR spectroscopy
UR - http://www.scopus.com/inward/record.url?scp=78650514824&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=78650514824&partnerID=8YFLogxK
U2 - 10.1007/s10072-010-0286-5
DO - 10.1007/s10072-010-0286-5
M3 - Article
C2 - 20464571
AN - SCOPUS:78650514824
VL - 31
SP - 799
EP - 805
JO - Neurological Sciences
JF - Neurological Sciences
SN - 1590-1874
IS - 6
ER -