TY - JOUR
T1 - A new case of idiopathic hemiplegia hemiconvulsion syndrome
AU - Franzoni, Emilio
AU - Garone, Caterina
AU - Marchiani, Valentina
AU - Brunetto, Daniela
AU - Tonon, Caterina
AU - Lodi, Raffaele
AU - Bernardi, Bruno
PY - 2010/12
Y1 - 2010/12
N2 - We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
AB - We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
KW - Epilepsy
KW - Hemiplegia hemiconvulsion
KW - MRI
KW - Proton MR spectroscopy
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U2 - 10.1007/s10072-010-0286-5
DO - 10.1007/s10072-010-0286-5
M3 - Article
C2 - 20464571
AN - SCOPUS:78650514824
VL - 31
SP - 799
EP - 805
JO - Neurological Sciences
JF - Neurological Sciences
SN - 1590-1874
IS - 6
ER -