TY - JOUR
T1 - A rare case of intravascular epithelioid hemangioendothelioma of the cephalic vein treated with surgery and postoperative radiation therapy
T2 - A case report and review of the literature
AU - Ciliberti, Maria Paola
AU - Caponio, Raffaella
AU - Pascali, Antonio
AU - Matichecchia, Gabriele
AU - Lioce, Marco
PY - 2015/4/29
Y1 - 2015/4/29
N2 - Introduction: Epithelioid hemangioendothelioma (EHE) is a rare endothelial tumor with an intermediate grade of malignancy. Few cases of primary vascular hemangioendothelioma have been described in the literature. Surgery is the treatment of choice, but radiation therapy and chemotherapy should also be considered in particular cases. Case presentation: We present the case of a 44-year-old Caucasian woman affected by EHE of the cephalic vein, treated by complete surgical removal of the mass and postoperative local radiation therapy. At 5-year follow-up, our patient is alive, with no signs of local or distant relapse and with no late radiation-related effects. Conclusions: Postoperative radiotherapy may play a role in cases in which tumor margins are close or cannot be assessed or when high-risk features are present.
AB - Introduction: Epithelioid hemangioendothelioma (EHE) is a rare endothelial tumor with an intermediate grade of malignancy. Few cases of primary vascular hemangioendothelioma have been described in the literature. Surgery is the treatment of choice, but radiation therapy and chemotherapy should also be considered in particular cases. Case presentation: We present the case of a 44-year-old Caucasian woman affected by EHE of the cephalic vein, treated by complete surgical removal of the mass and postoperative local radiation therapy. At 5-year follow-up, our patient is alive, with no signs of local or distant relapse and with no late radiation-related effects. Conclusions: Postoperative radiotherapy may play a role in cases in which tumor margins are close or cannot be assessed or when high-risk features are present.
KW - Cephalic vein
KW - Epithelioid hemangioendothelioma
KW - Intravascular
KW - Radiotherapy
KW - Review
KW - Vascular
UR - http://www.scopus.com/inward/record.url?scp=84934888274&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84934888274&partnerID=8YFLogxK
U2 - 10.1186/s13256-015-0565-0
DO - 10.1186/s13256-015-0565-0
M3 - Article
AN - SCOPUS:84934888274
VL - 9
JO - Journal of Medical Case Reports
JF - Journal of Medical Case Reports
SN - 1752-1947
IS - 1
M1 - 91
ER -