Adult syndrome: Dental features of a very rare condition

L Azzi, V Maurino, R Vinci, F Croveri, A Boggio, A Tagliabue, J Silvestre-Rangil, L Tettamanti

Research output: Contribution to journalArticle

Abstract

The Acro-Dermato-Ungual-Lacrimal-Tooth syndrome (ADULT syndrome) is one of the rarest ectodermal dysplasias and it is associated with several malformations involving especially the limbs. The most clinical features are the presence of ectrodactyly, syndactyly, hypermelanosis or multiple lentigines, onhycodysplasia, abnormalities in the lacrimal duct, recurrent conjuntivitis, photophobia, mammarian hypoplasia, hypotrichosis and frontal alopecia, hypohydrosis, cutaneous photosensitivity, nasal bridge prominence, exfoliative dermatitis and xerosis. The ectodermal dysfunction expresses itself with conoid teeth, enamel hypoplasia, dentinal dysplasia and especially hypodontia, with following functional and aesthetic defects. We report the case of an 11-year-old Caucasian girl affected by ADULT syndrome. © Copyright by BIOLIFE, s.a.s.
Original languageEnglish
Pages (from-to)61-65
Number of pages5
JournalJournal of Biological Regulators and Homeostatic Agents
Volume31
Issue number2, Suppl. 1
Publication statusPublished - 2017

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    Azzi, L., Maurino, V., Vinci, R., Croveri, F., Boggio, A., Tagliabue, A., Silvestre-Rangil, J., & Tettamanti, L. (2017). Adult syndrome: Dental features of a very rare condition. Journal of Biological Regulators and Homeostatic Agents, 31(2, Suppl. 1), 61-65. http://www.scopus.com/inward/record.url?scp=85031765461&partnerID=8YFLogxK