Abstract
Lymphangioleiomyomatosis and Langerhans cell Histiocytosis are two different diseases that can involve the lungs, with unknown etiology and origin. Both are rare, present a similar radiological pattern (multiple nodules and cysts in the lungs) and may have a similar clinical presentation, with progressive dyspnea, hemoptysis, pneumothorax and a variable course usually culminating in respiratory failure. Due to these similarities a differential diagnosis may be difficult in some instances. This review underlines differences in epidemiology, pathogenesis and prognosis that could assist clinicians in making a differential diagnosis of these rare and severe pulmonary diseases.
| Original language | English |
|---|---|
| Journal | Sarcoidosis Vasculitis and Diffuse Lung Diseases |
| Volume | 22 |
| Issue number | SUPPL. 1 |
| Publication status | Published - Dec 2005 |
Keywords
- Bronchoalveolar lavage
- Cystic lung diseases
- High-resolution computed tomography
- Langerhans cell histiocytosis
- Lymphangioleiomyomatosis
- Pulmonary arterial hypertension
- Pulmonary function tests
- Six-minute walking test
- Trans-bronchial biopsies
ASJC Scopus subject areas
- Pulmonary and Respiratory Medicine
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Cite this
Harari, S., & Paciocco, G. (2005). An integrated clinical approach to diffuse cystic lung diseases. Sarcoidosis Vasculitis and Diffuse Lung Diseases, 22(SUPPL. 1).