Anaesthetic management of a child with fibrodysplasia ossificans progressiva

Miriam Tumolo, A. Moscatelli, G. Silvestri

Research output: Contribution to journalArticle

18 Citations (Scopus)

Abstract

Fibrodysplasia Ossificans Progressiva (FOP) is a rare inherited disease in which progressive ossification of striated muscles leads to severe disability and respiratory impairment early in life and there are associated characteristic congenital skeletal malformations. Although this condition may prove demanding for the anaesthetist, few reports are available regarding anaesthesia in paediatric patients. We review the clinical features of the disease relevant to anaesthesia and describe the perioperative care of an 18-month-old boy with FOP who underwent endoscopic third-ventriculostomy for hydrocephalus associated with a brainstem mass. We emphasize the importance of an appropriate anaesthetic management of these patients, as inadequate care may lead to exacerbation of the disease with permanent sequelae.

Original languageEnglish
Pages (from-to)701-703
Number of pages3
JournalBritish Journal of Anaesthesia
Volume97
Issue number5
DOIs
Publication statusPublished - Nov 2006

Fingerprint

Myositis Ossificans
Anesthetics
Anesthesia
Ventriculostomy
Perioperative Care
Striated Muscle
Hydrocephalus
Rare Diseases
Osteogenesis
Brain Stem
Disease Progression
Pediatrics
Anesthetists

Keywords

  • Anaesthesia, paediatric
  • Complications, intubation tracheal
  • Equipment, bronchoscope
  • Fibrodysplasia ossificans progressiva

ASJC Scopus subject areas

  • Anesthesiology and Pain Medicine

Cite this

Anaesthetic management of a child with fibrodysplasia ossificans progressiva. / Tumolo, Miriam; Moscatelli, A.; Silvestri, G.

In: British Journal of Anaesthesia, Vol. 97, No. 5, 11.2006, p. 701-703.

Research output: Contribution to journalArticle

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