TY - JOUR
T1 - ... And if this was a Zinner's syndrome?
AU - Silveri, Massimiliano
AU - Zaccara, Antonio
AU - Colajacomo, Mauro
AU - Matarazzo, Ennio
AU - Diomedi Camassei, Francesca
AU - De Gennaro, Mario
PY - 2014
Y1 - 2014
N2 - A two year-old male was seen to our Emergency Department for acute abdominal pain, urinary retention and worsening constipation. A first level diagnostic imaging showed a pelvic cystic mass between bladder and rectum. Left kidney was absent. Further workup with MRI and endoscopy demonstrated the cyst to be of urogenital origin. Rapid increase in size and clinical symptoms prompted surgery. Pathology and surgical specimen showed the mass to be a left seminal vesicle cyst secondary to a malformation of the eiaculatory duct and embriologically related to ipsilateral renal agenesis. Such findings were consistent with the diagnosis of Zinner's syndrome (a clinical triad consisting of seminal vesicle cyst, ejaculatory duct obstruction and ipsilateral renal agenesis). Since the symptoms related to the seminal vesicle cyst coincide with the onset of a sexually active life, the majority of cases are generally observed and treated in the second and third decade. To our knowledge, this is the first case description in pediatric age.
AB - A two year-old male was seen to our Emergency Department for acute abdominal pain, urinary retention and worsening constipation. A first level diagnostic imaging showed a pelvic cystic mass between bladder and rectum. Left kidney was absent. Further workup with MRI and endoscopy demonstrated the cyst to be of urogenital origin. Rapid increase in size and clinical symptoms prompted surgery. Pathology and surgical specimen showed the mass to be a left seminal vesicle cyst secondary to a malformation of the eiaculatory duct and embriologically related to ipsilateral renal agenesis. Such findings were consistent with the diagnosis of Zinner's syndrome (a clinical triad consisting of seminal vesicle cyst, ejaculatory duct obstruction and ipsilateral renal agenesis). Since the symptoms related to the seminal vesicle cyst coincide with the onset of a sexually active life, the majority of cases are generally observed and treated in the second and third decade. To our knowledge, this is the first case description in pediatric age.
KW - Renal agenesis
KW - Seminal vesicle cyst
KW - Zinner's syndrome
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U2 - 10.1016/j.epsc.2014.10.018
DO - 10.1016/j.epsc.2014.10.018
M3 - Article
AN - SCOPUS:84912003612
VL - 2
SP - 530
EP - 532
JO - Journal of Pediatric Surgery Case Reports
JF - Journal of Pediatric Surgery Case Reports
SN - 2213-5766
IS - 12
ER -