Aortic surgery in Marfan patient with severe pectus excavatum

Giuseppe Maria Raffa, Mariusz Kowalewski, Pietro Giorgio Malvindi, Alessandro Bertani, Giuseppe Romano, Sergio Sciacca, Marco Turrisi, Alessandro Armaro, Vincenzo Stringi, Giuseppe Montalbano, Gabriella Mattiucci, Fabrizio Follis, Michele Pilato

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques. METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015. RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred. CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

Original languageEnglish
JournalJournal of Cardiovascular Medicine
DOIs
Publication statusE-pub ahead of print - Jun 30 2016

Fingerprint

Funnel Chest
Publications
Mortality
PubMed
MEDLINE
Aorta
Meta-Analysis
Dissection
Emergencies
Databases
Transplants
Phenotype

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

Cite this

@article{a6ada66e40d646d5806a0f2f2cb94caf,
title = "Aortic surgery in Marfan patient with severe pectus excavatum",
abstract = "AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques. METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015. RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred. CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.",
author = "Raffa, {Giuseppe Maria} and Mariusz Kowalewski and Malvindi, {Pietro Giorgio} and Alessandro Bertani and Giuseppe Romano and Sergio Sciacca and Marco Turrisi and Alessandro Armaro and Vincenzo Stringi and Giuseppe Montalbano and Gabriella Mattiucci and Fabrizio Follis and Michele Pilato",
year = "2016",
month = "6",
day = "30",
doi = "10.2459/JCM.0000000000000394",
language = "English",
journal = "Journal of Cardiovascular Medicine",
issn = "1558-2027",
publisher = "Lippincott Williams and Wilkins",

}

TY - JOUR

T1 - Aortic surgery in Marfan patient with severe pectus excavatum

AU - Raffa, Giuseppe Maria

AU - Kowalewski, Mariusz

AU - Malvindi, Pietro Giorgio

AU - Bertani, Alessandro

AU - Romano, Giuseppe

AU - Sciacca, Sergio

AU - Turrisi, Marco

AU - Armaro, Alessandro

AU - Stringi, Vincenzo

AU - Montalbano, Giuseppe

AU - Mattiucci, Gabriella

AU - Follis, Fabrizio

AU - Pilato, Michele

PY - 2016/6/30

Y1 - 2016/6/30

N2 - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques. METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015. RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred. CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

AB - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques. METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015. RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred. CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

UR - http://www.scopus.com/inward/record.url?scp=84965020896&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84965020896&partnerID=8YFLogxK

U2 - 10.2459/JCM.0000000000000394

DO - 10.2459/JCM.0000000000000394

M3 - Article

JO - Journal of Cardiovascular Medicine

JF - Journal of Cardiovascular Medicine

SN - 1558-2027

ER -