Abstract
AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.
METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.
RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.
CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.
| Original language | English |
|---|---|
| Pages (from-to) | 305-310 |
| Number of pages | 6 |
| Journal | Journal of Cardiovascular Medicine |
| Volume | 18 |
| Issue number | 5 |
| DOIs | |
| Publication status | Published - May 2017 |
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Keywords
- Adolescent
- Adult
- Aortic Aneurysm
- Blood Vessel Prosthesis Implantation
- Female
- Funnel Chest
- Humans
- Male
- Marfan Syndrome
- Middle Aged
- Orthopedic Procedures
- Risk Assessment
- Risk Factors
- Severity of Illness Index
- Sternum
- Treatment Outcome
- Young Adult
- Journal Article
- Meta-Analysis
- Review
Cite this
Aortic surgery in Marfan patients with severe pectus excavatum. / Raffa, Giuseppe Maria; Kowalewski, Mariusz; Malvindi, Pietro Giorgio; Bertani, Alessandro; Romano, Giuseppe; Sciacca, Sergio; Turrisi, Marco; Armaro, Alessandro; Stringi, Vincenzo; Montalbano, Giuseppe; Mattiucci, Gabriella; Follis, Fabrizio; Pilato, Michele.
In: Journal of Cardiovascular Medicine, Vol. 18, No. 5, 05.2017, p. 305-310.Research output: Contribution to journal › Review article
}
TY - JOUR
T1 - Aortic surgery in Marfan patients with severe pectus excavatum
AU - Raffa, Giuseppe Maria
AU - Kowalewski, Mariusz
AU - Malvindi, Pietro Giorgio
AU - Bertani, Alessandro
AU - Romano, Giuseppe
AU - Sciacca, Sergio
AU - Turrisi, Marco
AU - Armaro, Alessandro
AU - Stringi, Vincenzo
AU - Montalbano, Giuseppe
AU - Mattiucci, Gabriella
AU - Follis, Fabrizio
AU - Pilato, Michele
PY - 2017/5
Y1 - 2017/5
N2 - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.
AB - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.
KW - Adolescent
KW - Adult
KW - Aortic Aneurysm
KW - Blood Vessel Prosthesis Implantation
KW - Female
KW - Funnel Chest
KW - Humans
KW - Male
KW - Marfan Syndrome
KW - Middle Aged
KW - Orthopedic Procedures
KW - Risk Assessment
KW - Risk Factors
KW - Severity of Illness Index
KW - Sternum
KW - Treatment Outcome
KW - Young Adult
KW - Journal Article
KW - Meta-Analysis
KW - Review
U2 - 10.2459/JCM.0000000000000394
DO - 10.2459/JCM.0000000000000394
M3 - Review article
C2 - 27136701
VL - 18
SP - 305
EP - 310
JO - Journal of Cardiovascular Medicine
JF - Journal of Cardiovascular Medicine
SN - 1558-2027
IS - 5
ER -