Aortic surgery in Marfan patients with severe pectus excavatum

Giuseppe Maria Raffa; Mariusz Kowalewski; Pietro Giorgio Malvindi; Alessandro Bertani; Giuseppe Romano; Sergio Sciacca; Marco Turrisi; Alessandro Armaro; Vincenzo Stringi; Giuseppe Montalbano; Gabriella Mattiucci; Fabrizio Follis; Michele Pilato

doi:10.2459/JCM.0000000000000394

Aortic surgery in Marfan patients with severe pectus excavatum

Giuseppe Maria Raffa, Mariusz Kowalewski, Pietro Giorgio Malvindi, Alessandro Bertani, Giuseppe Romano, Sergio Sciacca, Marco Turrisi, Alessandro Armaro, Vincenzo Stringi, Giuseppe Montalbano, Gabriella Mattiucci, Fabrizio Follis, Michele Pilato

ISMETT

Research output: Contribution to journal › Review article › peer-review

Abstract

AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.

METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.

RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.

CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

Original language	English
Pages (from-to)	305-310
Number of pages	6
Journal	Journal of Cardiovascular Medicine
Volume	18
Issue number	5
DOIs	https://doi.org/10.2459/JCM.0000000000000394
Publication status	Published - May 2017

Keywords

Adolescent
Adult
Aortic Aneurysm
Blood Vessel Prosthesis Implantation
Female
Funnel Chest
Humans
Male
Marfan Syndrome
Middle Aged
Orthopedic Procedures
Risk Assessment
Risk Factors
Severity of Illness Index
Sternum
Treatment Outcome
Young Adult
Journal Article
Meta-Analysis
Review

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Aortic surgery in Marfan patients with severe pectus excavatum. / Raffa, Giuseppe Maria; Kowalewski, Mariusz; Malvindi, Pietro Giorgio; Bertani, Alessandro ; Romano, Giuseppe ; Sciacca, Sergio; Turrisi, Marco; Armaro, Alessandro; Stringi, Vincenzo; Montalbano, Giuseppe; Mattiucci, Gabriella; Follis, Fabrizio; Pilato, Michele.

In: Journal of Cardiovascular Medicine, Vol. 18, No. 5, 05.2017, p. 305-310.

Research output: Contribution to journal › Review article › peer-review

Raffa, Giuseppe Maria ; Kowalewski, Mariusz ; Malvindi, Pietro Giorgio ; Bertani, Alessandro ; Romano, Giuseppe ; Sciacca, Sergio ; Turrisi, Marco ; Armaro, Alessandro ; Stringi, Vincenzo ; Montalbano, Giuseppe ; Mattiucci, Gabriella ; Follis, Fabrizio ; Pilato, Michele. / Aortic surgery in Marfan patients with severe pectus excavatum. In: Journal of Cardiovascular Medicine. 2017 ; Vol. 18, No. 5. pp. 305-310.

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abstract = "AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.",

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author = "Raffa, {Giuseppe Maria} and Mariusz Kowalewski and Malvindi, {Pietro Giorgio} and Alessandro Bertani and Giuseppe Romano and Sergio Sciacca and Marco Turrisi and Alessandro Armaro and Vincenzo Stringi and Giuseppe Montalbano and Gabriella Mattiucci and Fabrizio Follis and Michele Pilato",

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AU - Raffa, Giuseppe Maria

AU - Kowalewski, Mariusz

AU - Malvindi, Pietro Giorgio

AU - Bertani, Alessandro

AU - Romano, Giuseppe

AU - Sciacca, Sergio

AU - Turrisi, Marco

AU - Armaro, Alessandro

AU - Stringi, Vincenzo

AU - Montalbano, Giuseppe

AU - Mattiucci, Gabriella

AU - Follis, Fabrizio

AU - Pilato, Michele

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N2 - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

AB - AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.

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