Abstract
AIMS: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques.
METHODS: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015.
RESULTS: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred.
CONCLUSION: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality.
Original language | English |
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Pages (from-to) | 305-310 |
Number of pages | 6 |
Journal | Journal of Cardiovascular Medicine |
Volume | 18 |
Issue number | 5 |
DOIs | |
Publication status | Published - May 2017 |
Keywords
- Adolescent
- Adult
- Aortic Aneurysm
- Blood Vessel Prosthesis Implantation
- Female
- Funnel Chest
- Humans
- Male
- Marfan Syndrome
- Middle Aged
- Orthopedic Procedures
- Risk Assessment
- Risk Factors
- Severity of Illness Index
- Sternum
- Treatment Outcome
- Young Adult
- Journal Article
- Meta-Analysis
- Review