Atrial septal aneurysm in a patient with pseudoxanthoma elasticum

Giuseppe Bertulezzi, Riccardo Paris, Mauro Moroni, Camille Porta, Giuseppe Nastasi, Amedeo Amadeo

Research output: Contribution to journalArticlepeer-review


Pseudoxanthoma elasticum (PXE) is a rare heritable disorder of the connective tissue characterized by marked clinical heterogeneity. Common cardiovascular complications of PXE include renovascular hypertension, premature coronary artery disease and calcification of peripheral arteries frequently leading to claudicatio intermittens; fibrous thickening of the endocardium and atrioventricular valves, leading to restrictive cardiomyopathy and/or mitral valve prolapse have been also described. We herein report on a PXE patient who developed an atrial septal aneurysm as a previously undescribed cardiologic manifestation of her disease.

Original languageEnglish
Pages (from-to)223-225
Number of pages3
JournalActa Cardiologica
Issue number4
Publication statusPublished - 1998


  • Atrial septal aneurysm
  • Cardiovascular complication
  • Case report
  • PXE

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine


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