Band heterotopia is a neuronal migration disorder which consists of a symmetrical subcortical neuronal band. We describe two girls who had band heterotopia and Lennox-Gastaut syndrome (LGS); both patients had severe mental retardation, atonic seizures, a typical absences and tonic seizures. MR images showed in both girls an identical subcortical symmetrical layer isointense with gray matter. The association of a LGS with 'double cortex' suggests that this neuronal migration anomaly may be responsible for other cases of LGS.
|Translated title of the contribution||Band heterotopia: A diffuse neuronal migration anomaly as a cause of the Lennox-Gastaut syndrome|
|Number of pages||3|
|Journal||Bollettino - Lega Italiana contro l'Epilessia|
|Publication status||Published - 1991|
ASJC Scopus subject areas
- Clinical Neurology