Biliary atresia associated with multiple unrelated anomalies: What about it?

G. Casaccia, O. A. Catalano, M. Marcellini, P. Bagolan

Research output: Contribution to journalArticle

Abstract

The prognosis of extrahepatic biliary atresia (EHBA) and multiple apparently not linked anomalies has never been disclosed. We reported a rare case affected by biliary, anorectal and esophageal atresia, and collected the uncommon associations of EHBA with multiple unrelated congenital defects to make known the prognosis. An elevated rate of hepatic failure despite surgery and an early poor outcome were found in the above-mentioned associations. A liver transplantation at the first months of life could be considered to improve outcome.

Original languageEnglish
Pages (from-to)277-280
Number of pages4
JournalPediatric Surgery International
Volume23
Issue number3
DOIs
Publication statusPublished - Mar 2007

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Biliary Atresia
Esophageal Atresia
Liver Failure
Liver Transplantation

Keywords

  • Extrahepatic biliary atresia
  • Malformations
  • Outcome
  • Perinatal form
  • Syndromes

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

Biliary atresia associated with multiple unrelated anomalies : What about it? / Casaccia, G.; Catalano, O. A.; Marcellini, M.; Bagolan, P.

In: Pediatric Surgery International, Vol. 23, No. 3, 03.2007, p. 277-280.

Research output: Contribution to journalArticle

Casaccia, G. ; Catalano, O. A. ; Marcellini, M. ; Bagolan, P. / Biliary atresia associated with multiple unrelated anomalies : What about it?. In: Pediatric Surgery International. 2007 ; Vol. 23, No. 3. pp. 277-280.
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