Biventricular pacing in an infant with noncompaction of the ventricular myocardium, congenital AV block, and prolonged QT interval

Fabrizio Drago, Massimo Stefano Silvetti, Marco Annichiarico, Guido Michielon, Gianluca Brancaccio, Stefano Zanoni, Sergio Valsecchi

Research output: Contribution to journalArticle

Abstract

We describe the case of a newborn with isolated noncompaction of the ventricular myocardium, congenital atrioventricular block, and prolonged QT, who developed a dilated cardiomyopathy after 4 months of right ventricular permanent pacing. The implanted system was upgraded to biventricular pacing. Resynchronization therapy was associated with normalized septal motion and shortening of the interventricular delay and, within 2 months after initiation, resulted in markedly improved left ventricular ejection fraction and reduced ventricular volume.

Original languageEnglish
Pages (from-to)67-70
Number of pages4
JournalJournal of Interventional Cardiac Electrophysiology
Volume28
Issue number1
DOIs
Publication statusPublished - Jun 2010

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Isolated Noncompaction of the Ventricular Myocardium
Cardiac Resynchronization Therapy
Atrioventricular Block
Dilated Cardiomyopathy
Stroke Volume
Myocardium
Newborn Infant
Therapeutics

Keywords

  • Congenital atrioventricular block
  • CRT
  • Dilated cardiomyopathy
  • Noncompacted ventricular myocardium
  • Pediatrics

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Physiology (medical)

Cite this

Biventricular pacing in an infant with noncompaction of the ventricular myocardium, congenital AV block, and prolonged QT interval. / Drago, Fabrizio; Silvetti, Massimo Stefano; Annichiarico, Marco; Michielon, Guido; Brancaccio, Gianluca; Zanoni, Stefano; Valsecchi, Sergio.

In: Journal of Interventional Cardiac Electrophysiology, Vol. 28, No. 1, 06.2010, p. 67-70.

Research output: Contribution to journalArticle

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