Brainstem auditory evoked responses in Lafora disease

U. Aguglia, G. Farnarier, P. Tinuper, A. Quattrone

Research output: Contribution to journalArticle


Brainstem auditory-evoked responses (BAERs) have been studied in five patients suffering from Lafora-type of progressive myoclonus epilepsy proven by skin biopsy and in ten healthy volunteers. At the time of examination the patients were not taking benzodiazepines and showed myoclonic jerks. In all patients the central conduction time (interpeak latencies I-V, I-III, III-V) and the amplitude (amplitude ratio I/V) of BAERs were within the ±2 S.D. limits of the normal values. Since Lafora disease is a neuropathologically prevalent grey-matter illness (typical inclusion bodies are stored intraneuronally) these data indicate that diseases primarily affecting the brainstem grey-matter are usually associated with normal BAERs.

Original languageEnglish
Pages (from-to)202-207
Number of pages6
JournalClinical EEG Electroencephalography
Issue number4
Publication statusPublished - 1985

ASJC Scopus subject areas

  • Clinical Neurology

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    Aguglia, U., Farnarier, G., Tinuper, P., & Quattrone, A. (1985). Brainstem auditory evoked responses in Lafora disease. Clinical EEG Electroencephalography, 16(4), 202-207.