Abstract
The autonomic nervous system has been evaluated in myotonic dystrophy with contradictory results and its relationship with heart disturbances remains unclear. Twenty-three patients with myotonic dystrophy type 1 were investigated by a battery of six cardiovascular autonomic tests and power spectral analysis of heart rate variability. Although 15 patients (65%) revealed abnormal or borderline results in some tests, only one patient had a definite autonomic damage, as indicated by two or more abnormal tests. As a group, myotonic dystrophy type 1 patients showed a significant reduction of heart rate variability during deep breathing (P
Original language | English |
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Pages (from-to) | 136-141 |
Number of pages | 6 |
Journal | Neuromuscular Disorders |
Volume | 14 |
Issue number | 2 |
DOIs | |
Publication status | Published - Feb 2004 |
Keywords
- Autonomic nervous system
- Cardiovascular reflex tests
- Heart disturbances
- Heart rate variability
- Myotonic dystrophy type 1
- Power spectral analysis
ASJC Scopus subject areas
- Clinical Neurology
- Pediatrics, Perinatology, and Child Health
- Developmental Neuroscience
- Neurology