Chiari complex in children - Neuroradiological diagnosis, neurosurgical treatment and proposal of a new classification (312 cases)

A. Cama, P. Tortori-Donati, G. L. Piatelli, M. P. Fondelli, L. Andreussi

Research output: Contribution to journalArticle

51 Citations (Scopus)

Abstract

Chiari malformations are a group of anomalies particularly involving the hindbrain and cervical spinal cord. Since these malformations present many common features, we called them 'Chiari Complex'. After reviewing our 312 patients affected by different types of Chiari malformations we propose the following classification: Chiari I (30 cases): 1) This malformation may be divided in two sub-types: a) classic and b) myelencephalic forms. 2) Only three children were admitted with specific clinical symptoms and they had an occipito-cervical surgical decompression. Chiari II (276 cases): 1) Most of our patients (70%) presented with progressive hydrocephalus and they needed a CSF shunt to be inserted. 2) Seven sub-types of 4th ventricle morphology and size were identified. 3) Only 11 patients underwent a cervical decompression; in 182 children CSF shunting resulted in a good clinical outcome. Chiari III (2 cases): Chiari II signs must be associated with an occipito-cervical cephalocele. In both cases there were other severe associated CNS malformations. Chiari IV (4 cases): We propose this name for patients with myelomeningocele (MMC) and severe cerebellar hypoplasia.

Original languageEnglish
Pages (from-to)35-38
Number of pages4
JournalEuropean Journal of Pediatric Surgery
Volume5
Issue numberSUPPL. 1
Publication statusPublished - 1995

Fingerprint

Encephalocele
Fourth Ventricle
Surgical Decompression
Meningomyelocele
Rhombencephalon
Therapeutics
Hydrocephalus
Decompression
Names
Cerebellar Hypoplasia
Cervical Cord

Keywords

  • Chiari malformation
  • Myelomeningocele
  • Neural tube defect

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

Chiari complex in children - Neuroradiological diagnosis, neurosurgical treatment and proposal of a new classification (312 cases). / Cama, A.; Tortori-Donati, P.; Piatelli, G. L.; Fondelli, M. P.; Andreussi, L.

In: European Journal of Pediatric Surgery, Vol. 5, No. SUPPL. 1, 1995, p. 35-38.

Research output: Contribution to journalArticle

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