Cochlear Implantation as a Treatment for Sudden Autoimmune Sensorineural Hearing Loss in a Patient Affected by Eosinophilic Granulomatosis with Polyangiitis: A Case Report and A Review of Literature

Tommaso Cacco, Eolo Castello, Frank Rikki Mauritz Canevari, Andrea Laborai, Alessandra Grillone, Diego Zanetti, Giorgio Peretti

Research output: Contribution to journalArticlepeer-review

Abstract

Objective: To report presentation, diagnostic process, management and outcome of a case of autoimmune inner ear disease (AIED) related with Churg-Strauss syndrome, also known as eosinophilic granulomatosis with polyangiitis (EGPA), treated with cochlear implantation, and review of relevant literature. Case presentation and management: A retrospective case report of AIED associated with EGPA treated with cochlear implantation was described. A multi-step approach for diagnosis and confirmation of AIED and hearing rehabilitation was conducted, eventually leading to left cochlear implantation. Results: The surgery was without complications and postoperative course was uneventful. Two years after surgery, pure-tone and speech soundfield audiometry with left cochlear implant switched on showed a good improvement in pure-tone threshold and a word recognition score of 50% at 60 dB nHL. Literature review does not report any previous case of AIED EGPA-related. Conclusions: Cochlear implantation in AIED EGPA-related have been shown to be a viable treatment option in a stabilized phase of disease.

Original languageEnglish
Pages (from-to)112-115
JournalAnnals of Otology, Rhinology and Laryngology
Volume130
Issue number1
DOIs
Publication statusPublished - 2021

Keywords

  • audiology
  • autoimmune hearing loss
  • Churg-Strauss syndrome
  • cochlear implantation
  • sudden hearing loss

ASJC Scopus subject areas

  • Otorhinolaryngology

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