Congenital intrahepatic portohepatic shunt managed by interventional radiologic occlusion: A case report and literature review

Chiara Grimaldi, Lidia Monti, Piergiorgio Falappa, Giuseppe D'Ambrosio, Antonio Manca, Jean De Ville De Goyet

Research output: Contribution to journalArticle

Abstract

Congenital intrahepatic portosystemic shunts are rare hepatic vascular anomalies that often lead to severe secondary conditions. A 6-year-old boy was referred for assessment of severe hypoxia, and a large liver mass was diagnosed with such a malformation and was managed by direct closure of the venous fistula by interventional radiology. Follow-up assessment shows normalization of the respiratory condition and a progressive reduction of the vascular liver lesion. Review of literature suggests that radiologic interventions are currently the criterion standard for managing these conditions, with surgery reserved for patients who are not eligible for radiologic procedure and those requiring liver transplantation.

Original languageEnglish
JournalJournal of Pediatric Surgery
Volume47
Issue number2
DOIs
Publication statusPublished - Feb 2012

Keywords

  • Congenital malformation
  • Hepatopulmonary syndrome
  • Interventional radiology
  • Liver anatomy
  • Portosystemic shunt

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

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