The authors followed up 9 cases of congenital pseudoarthrosis associated with neurofibromatosis-1 (or Von Recklinghausen's disease) at least 2 years after the end of treatment using Ilizarov's method. All patients, except one, had previously undergone one or more operations using traditional techniques. Three types of device were used: a) direct compression of pseudoarthrosis stumps; b) extensive resection of stumps, their immediate compression and proximal metaphyseal corticotomy to compensate dysmetry; c) 'lift' technique. The following were evaluated: 1) immediate results: consolidation of pseud0arthrosis (7 cases out of 9) in relation to level, anatomopathological type and device used; 2) onset of fractures or axial deviations within the first 2 years of removal of fixator (3 axial deviations and 3 fractures) and their treatment; 3) long-term results: 45% of consolidation. In conclusion, the authors affirm that, while Ilizarov's method is able to improve the prognosis of congenital pseudoarthrosis in neurofibromatosis-1, it does not allow a reliable recovery to be made in all patients. Prognosis continues to be reserved especially in clepsydra forms and those localised to the lower third of the tibia.
|Translated title of the contribution||Congenital pseudoarthrosis of the tibia: Treatment using Ilizarov device|
|Number of pages||6|
|Journal||Minerva Ortopedica e Traumatologica|
|Publication status||Published - 1996|
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