Congenital, solitary, large, intrahepatic arterioportal fistula in a child: Management and review of the literature

Nagappan Kumar, Jean de Ville de Goyet, Khalid Sharif, Patrick McKiernan, Philip John

Research output: Contribution to journalArticle

Abstract

Congenital intrahepatic arterioportal fistula (APF) is a rare condition. In most cases, the symptoms and complications develop during infancy. We report here the incidental finding of a large and solitary congenital APF in a 13-year-old boy, with subsequent related clinical complications. At angiography, an APF connecting the left hepatic artery and the left branch of the portal vein (PV) was demonstrated with reversed flow in the left and main PV. The fistula was successfully occluded, in a single embolisation session, using an Amplatzer occlusion device. This was associated with immediate restoration of normal hepatopetal flow in the PV and followed by resolution of the clinical signs of portal hypertension. This patient is the oldest child with congenital intrahepatic APF to be reported. We emphasise the interest of using a large device (Amplatzer) to occlude a solitary large APF in a single session and, more importantly, to avoid other possible complications related to embolisation.

Original languageEnglish
Pages (from-to)20-23
Number of pages4
JournalPediatric Radiology
Volume33
Issue number1
DOIs
Publication statusPublished - Jan 1 2003

Keywords

  • Arterioportal fistula
  • Congenital vascular malformation
  • Liver
  • Portal hypertension
  • Radiological intervention

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Pediatrics, Perinatology, and Child Health
  • Radiological and Ultrasound Technology

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