Cutaneous angiosarcoma in a patient with xeroderma pigmentosum

Research output: Contribution to journalArticle

Abstract

Xeroderma pigmentosum (XP) is a DNA repair defect syndrome associated with an increased risk to developing skin neoplasms on sun-exposed cutaneous surfaces. This report describes the case of a 15-year-old boy with XP who developed cutaneous angiosarcoma. The patient was cured with surgery alone, despite incomplete resection, and he is alive without evidence of disease 40 months after diagnosis. It is the fourth reported case-and the third in pediatric age-of the association of XP with this soft part sarcoma.

Original languageEnglish
Pages (from-to)23-26
Number of pages4
JournalPediatric Hematology and Oncology
Volume21
Issue number1
DOIs
Publication statusPublished - Jan 2004

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Keywords

  • Cutaneous angiosarcoma
  • Xeroderma pigmentosum

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Hematology
  • Oncology
  • Cancer Research
  • Management of Technology and Innovation

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