Dermatomyositis (DM) is an idiopathic inflammatory myopathy characterised by a variety of cutaneous findings; Gottron's papules, usually occurring on the dorsal surface of metacarpophalangeal and interphalangeal joints, are the typical cutaneous lesion presented by these patients. Other cutaneous findings are heliotrope rash, a violaceous macular erythema of the eyelids, and mechanic's hands, a darkened, or dirty-appearing, horizontal lines across the fingers. On the other hand DM had been associated with different cutaneous manifestations like poikiloderma atrophicans vasculare flagellate erythema, scleromyxedema, cuticular erythema, vasculitis, necrotic ulcers, calcinosis, lipodistropby. In literature cases with typical cutaneous manifestations of DM but without any sign of muscular involvement had been reported; this subset of disease is called amyopathic DM. Other particular subsets of the disease are Wong's DM and antisynthetase syndrome; the first one is characterised by the occurrence of lesions similar to pityriasis rubra pilaris, whereas the latter is strictly associated with the occurrence of interstitial lung disease, arthritis positivity of antisyntethase antibodies and the presence of mechanic's hands. With this paper we want to review the different cutaneous findings of DM subsets, with particular regard to amyopathic DM, Wong's DM and antisynthetase syndrome.
|Number of pages||10|
|Journal||Progressi in Reumatologia|
|Publication status||Published - 2003|
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