Cutaneous mucinosis of infancy: Is it a real entity or the paediatric form of lichen myxoedematosus (papular mucinosis)?

M. Podda, Franco Rongioletti, D. Greiner, R. Milbradt, A. Rebora, R. Kaufmann, M. Wolter

Research output: Contribution to journalArticle

22 Citations (Scopus)

Abstract

We describe a girl presenting with a childhood dermal mucinosis in which we had the unique opportunity to find all the transitional histological features of lichen myxoedematosus (papular mucinosis), from its early focal mucin deposition in the reticular dermis to its late findings of interstitial mucin deposition, dermal fibrosis and fibroblast proliferation. Her father reported having had similar lesions when he was a child, which completely disappeared during adolescence. This case, and a re-evaluation of the literature, suggests that cases of cutaneous mucinosis of infancy that are not hamartomatous conditions such as mucinous naevi are in fact the infantile presentation of lichen myxoedematosus (papular mucinosis) and, in addition to other cases in the literature, suggests a genetic and familial factor in lichen myxoedematosus (papular mucinosis).

Original languageEnglish
Pages (from-to)590-593
Number of pages4
JournalBritish Journal of Dermatology
Volume144
Issue number3
DOIs
Publication statusPublished - 2001

Fingerprint

Mucinoses
Scleromyxedema
Lichens
Mucins
Pediatrics
Skin
Nevus
Dermis
Fathers
Fibrosis
Fibroblasts

Keywords

  • Cutaneous mucinosis of infancy
  • Lichen myxoedematosus
  • Mucinous naevus
  • Papular mucinosis

ASJC Scopus subject areas

  • Dermatology

Cite this

Cutaneous mucinosis of infancy : Is it a real entity or the paediatric form of lichen myxoedematosus (papular mucinosis)? / Podda, M.; Rongioletti, Franco; Greiner, D.; Milbradt, R.; Rebora, A.; Kaufmann, R.; Wolter, M.

In: British Journal of Dermatology, Vol. 144, No. 3, 2001, p. 590-593.

Research output: Contribution to journalArticle

Podda, M. ; Rongioletti, Franco ; Greiner, D. ; Milbradt, R. ; Rebora, A. ; Kaufmann, R. ; Wolter, M. / Cutaneous mucinosis of infancy : Is it a real entity or the paediatric form of lichen myxoedematosus (papular mucinosis)?. In: British Journal of Dermatology. 2001 ; Vol. 144, No. 3. pp. 590-593.
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