Abstract
We describe a girl presenting with a childhood dermal mucinosis in which we had the unique opportunity to find all the transitional histological features of lichen myxoedematosus (papular mucinosis), from its early focal mucin deposition in the reticular dermis to its late findings of interstitial mucin deposition, dermal fibrosis and fibroblast proliferation. Her father reported having had similar lesions when he was a child, which completely disappeared during adolescence. This case, and a re-evaluation of the literature, suggests that cases of cutaneous mucinosis of infancy that are not hamartomatous conditions such as mucinous naevi are in fact the infantile presentation of lichen myxoedematosus (papular mucinosis) and, in addition to other cases in the literature, suggests a genetic and familial factor in lichen myxoedematosus (papular mucinosis).
| Original language | English |
|---|---|
| Pages (from-to) | 590-593 |
| Number of pages | 4 |
| Journal | British Journal of Dermatology |
| Volume | 144 |
| Issue number | 3 |
| DOIs | |
| Publication status | Published - 2001 |
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Keywords
- Cutaneous mucinosis of infancy
- Lichen myxoedematosus
- Mucinous naevus
- Papular mucinosis
ASJC Scopus subject areas
- Dermatology
Cite this
Cutaneous mucinosis of infancy : Is it a real entity or the paediatric form of lichen myxoedematosus (papular mucinosis)? / Podda, M.; Rongioletti, Franco; Greiner, D.; Milbradt, R.; Rebora, A.; Kaufmann, R.; Wolter, M.
In: British Journal of Dermatology, Vol. 144, No. 3, 2001, p. 590-593.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Cutaneous mucinosis of infancy
T2 - Is it a real entity or the paediatric form of lichen myxoedematosus (papular mucinosis)?
AU - Podda, M.
AU - Rongioletti, Franco
AU - Greiner, D.
AU - Milbradt, R.
AU - Rebora, A.
AU - Kaufmann, R.
AU - Wolter, M.
PY - 2001
Y1 - 2001
N2 - We describe a girl presenting with a childhood dermal mucinosis in which we had the unique opportunity to find all the transitional histological features of lichen myxoedematosus (papular mucinosis), from its early focal mucin deposition in the reticular dermis to its late findings of interstitial mucin deposition, dermal fibrosis and fibroblast proliferation. Her father reported having had similar lesions when he was a child, which completely disappeared during adolescence. This case, and a re-evaluation of the literature, suggests that cases of cutaneous mucinosis of infancy that are not hamartomatous conditions such as mucinous naevi are in fact the infantile presentation of lichen myxoedematosus (papular mucinosis) and, in addition to other cases in the literature, suggests a genetic and familial factor in lichen myxoedematosus (papular mucinosis).
AB - We describe a girl presenting with a childhood dermal mucinosis in which we had the unique opportunity to find all the transitional histological features of lichen myxoedematosus (papular mucinosis), from its early focal mucin deposition in the reticular dermis to its late findings of interstitial mucin deposition, dermal fibrosis and fibroblast proliferation. Her father reported having had similar lesions when he was a child, which completely disappeared during adolescence. This case, and a re-evaluation of the literature, suggests that cases of cutaneous mucinosis of infancy that are not hamartomatous conditions such as mucinous naevi are in fact the infantile presentation of lichen myxoedematosus (papular mucinosis) and, in addition to other cases in the literature, suggests a genetic and familial factor in lichen myxoedematosus (papular mucinosis).
KW - Cutaneous mucinosis of infancy
KW - Lichen myxoedematosus
KW - Mucinous naevus
KW - Papular mucinosis
UR - http://www.scopus.com/inward/record.url?scp=0035078292&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0035078292&partnerID=8YFLogxK
U2 - 10.1046/j.1365-2133.2001.04090.x
DO - 10.1046/j.1365-2133.2001.04090.x
M3 - Article
C2 - 11260021
AN - SCOPUS:0035078292
VL - 144
SP - 590
EP - 593
JO - British Journal of Dermatology
JF - British Journal of Dermatology
SN - 0007-0963
IS - 3
ER -