The Authors report a 30-year-old man presented with a 3 years history of a 10 x 5 cm plaque-like area of red discoloration on the anterior abdominal wall. The patient reported an antecedent trauma with a crossbow in the site of tumor. The histological examination revealed a dermatofibrosarcoma protuberans (DFSP) composed predominantly of cells with large, spindle-shaped nuclei, offering a fairly uniform aspect. The cells were arranged in irregular, intertwining bands, resulting in a storiform pattern. The DFSP is a locally aggressive neoplasm that recurs in up to half of the patients. The risk of local recurrence, furthermore, correlates well with the extent of the wide excision. Despite the locally aggressive behavior this tumor infrequently metastasizes. DSFP, first described in 1924 by Darier and Ferrand as "progressive and recurring dermatofibroma", is a nodular cutaneous tumor characterized by a prominent storiform pattern. Over the years it has been considered a fibroblastic, histiocytic and even a neural tumor, and to date there is no general consensus concerning its histogenesis. DFSP typically presents during early or mid-adult life as a nodular cutaneous mass. Although this tumor may occur at almost any site, this is most frequent on the trunk and proximal extremities.
|Translated title of the contribution||Dermatofibrosarcoma protuberans: A case report with unusual genesis|
|Publication status||Published - 1997|
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