Dermochondrocorneal Dystrophy (François' Syndrome): Report of a Case

Ruggero Caputo, Niccla Sambvani, Marcello Monti, Stefano Cavicchini, Antonio Carrassi, Roberto Ratiglia

Research output: Contribution to journalArticlepeer-review

Abstract

Dermochondrocorneal dystrophy (François' syndrome) is an extremely rare disorder characterized by firm, nodular lesions involving the hands and the face; osteochondrodystrophy of the peripheral extremital bones, resulting in limitation of movement; and corneal dystrophy marked by white or brownish opacities. A nonfamilial case of dermochondrocorneal dystrophy was studied in a 45-year-old woman who had severe involvement of the gingival and palatal mucous membranes.

Original languageEnglish
Pages (from-to)424-428
Number of pages5
JournalArchives of Dermatology
Volume124
Issue number3
DOIs
Publication statusPublished - 1988

ASJC Scopus subject areas

  • Dermatology

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