Double-Outlet Right Atrium: Anatomic and Clinical Considerations

Gianluca Brancaccio, Antonio Amodeo, Gabriele Rinelli, Sergio Filippelli, Stephen P. Sanders, Roberto M. Di Donato

Research output: Contribution to journalArticlepeer-review

Abstract

Background: Double-outlet right atrium (DORA) is a condition in which the right atrium empties into both ventricles. Described are the anatomic and clinical findings of this rare anomaly and our experience with its surgical treatment. Methods: A retrospective review was conducted of all medical records and two-dimensional echocardiographic assessments, and the operative reports of patients with DORA were reexamined to identify the specific anatomic features and the relative adaptation of surgical technique. Results: From January 1983 to November 2004, 12 patients with DORA underwent surgical treatment. The diagnosis was made in all cases by two-dimensional echocardiography. All patients had mild-to-moderate signs of arterial oxygen desaturation. All patients also had either a partial (n = 11) or a complete (n = 1) atrioventricular canal with or without other associated cardiac anomalies, including persistent left superior vena cava. Eleven patients survived the surgical repair, the only death occurred in a patient with Ellis Von-Creveld syndrome, with multiple skeletal malformations, severe chest hypoplasia, and respiratory distress. Conclusions: DORA is a rare and peculiar cardiac anomaly with well-defined characteristics. Its recognition, best achieved by two-dimensional echocardiography, is crucial for a good surgical correction.

Original languageEnglish
Pages (from-to)619-621
Number of pages3
JournalAnnals of Thoracic Surgery
Volume83
Issue number2
DOIs
Publication statusPublished - Feb 2007

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Surgery

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