The authors describe for the first time in literature two cases of double outlet right atrium. Both were associated with a complete Atrio Ventricular Canal (A.V.C.); Double Outlet Right Ventricle (D.O.R.V.) was associated, too. In both cases, the anatomy - pathological peculiarity was the communication of the rightatrium with the two A-V cardiac valves. The left atrium, which was in communication with the left auricle, had got an oval closing hole as its only way of exit. The malformation is the anatomic symmetric painting of the malformation delineated for the first time by Horiuchi and Coll. and called double outlet left atrium associated with A.V.C. and D.O.R.V. Both cases in the article have had a surgical correction in E.C.C. We have had a good result in the case of a 10 yr old girl; the other case, a 4 mth old child with a D.O.R.V. associated, died. The correction of the malformation has been the making of a tunnel between the left atrium and the mitral valve after the enlargement of the oval hole. Embryologically, the atrial septum primum is displaced to the left hand fused with the right margin of the atrioventricular (A-V) canal rather than growing to the center of the dividing A-V canal.
|Translated title of the contribution||Double outlet right atrium with complete A-V canal: Anatomic and clinical features in the first two cases|
|Number of pages||5|
|Journal||Pediatria Medica e Chirurgica|
|Publication status||Published - 1979|
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health