Early onset benign occipital susceptibility syndrome: Video-EEG documentation of an illustrative case

Federico Vigevano, Maria Luisa Lispi, Stefano Ricci

Research output: Contribution to journalArticle

Abstract

Early onset benign occipital susceptibility syndrome (EBOSS) is a recently delineated form of idiopathic childhood partial epilepsy, which is still not recognized by the International League Against Epilepsy as a distinct epileptic syndrome. It occurs with generally nocturnal, prolonged partial seizures, which can become a status epilepticus. The seizures are characterized by tonic eye deviation, vomiting, progressive impairment of consciousness, autonomic symptoms, frequent progression to hemiconvulsions or generalized tonic-clonic seizures. Age at onset is usually between 3 and 7 years, frequency is remarkably low (often a single seizure), and outcome is excellent. Interictal EEG shows occipital paroxysms with fixation-off sensitivity. We present the first video-EEG documentation of typical case of EBOSS and discuss the clinical and EEG features of the case. The documentation is useful for a better definition of the syndrome and also permits a differential diagnosis with respect to other occipital forms of epilepsy and other sleep related paroxysmal disorders. (C) 2000 Elsevier Science Ireland Ltd.

Original languageEnglish
JournalClinical Neurophysiology
Volume111
Issue numberSUPPL. 2
DOIs
Publication statusPublished - Sep 1 2000

Keywords

  • Idiopathic localization-related epilepsy
  • Nocturnal seizures
  • Occipital paroxysms
  • Occipital seizures
  • Video-EEG recording

ASJC Scopus subject areas

  • Clinical Neurology
  • Physiology (medical)
  • Radiology Nuclear Medicine and imaging
  • Neurology
  • Sensory Systems

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