Abstract
Early onset benign occipital susceptibility syndrome (EBOSS) is a recently delineated form of idiopathic childhood partial epilepsy, which is still not recognized by the International League Against Epilepsy as a distinct epileptic syndrome. It occurs with generally nocturnal, prolonged partial seizures, which can become a status epilepticus. The seizures are characterized by tonic eye deviation, vomiting, progressive impairment of consciousness, autonomic symptoms, frequent progression to hemiconvulsions or generalized tonic-clonic seizures. Age at onset is usually between 3 and 7 years, frequency is remarkably low (often a single seizure), and outcome is excellent. Interictal EEG shows occipital paroxysms with fixation-off sensitivity. We present the first video-EEG documentation of typical case of EBOSS and discuss the clinical and EEG features of the case. The documentation is useful for a better definition of the syndrome and also permits a differential diagnosis with respect to other occipital forms of epilepsy and other sleep related paroxysmal disorders. (C) 2000 Elsevier Science Ireland Ltd.
Original language | English |
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Journal | Clinical Neurophysiology |
Volume | 111 |
Issue number | SUPPL. 2 |
DOIs | |
Publication status | Published - Sep 1 2000 |
Keywords
- Idiopathic localization-related epilepsy
- Nocturnal seizures
- Occipital paroxysms
- Occipital seizures
- Video-EEG recording
ASJC Scopus subject areas
- Clinical Neurology
- Physiology (medical)
- Radiology Nuclear Medicine and imaging
- Neurology
- Sensory Systems