Esordio precoce di una neoplasia nasale a cellule epiteliodi perivascolari non associata a sclerosi tuberosa

Translated title of the contribution: Early onset of a nasal perivascular epithelioid cell neoplasm not related to tuberous sclerosis complex

S. Gana, P. Morbini, G. Giourgos, E. Matti, F. Chu, C. Danesino, F. Pagella

Research output: Contribution to journalArticle

Abstract

Perivascular epithelioid cell neoplasms are a group of rare tumours reported in various organs under a variety of designations. Such tumours are of interest primarily because of the distinctive morphology of their cell population and their immunoreactivity with melanocytic and myoid markers. There is a strong association between perivascular epithelioid cell neoplasms and tuberous sclerosis complex. Perivascular epithelioid cell neoplasms very rarely occur in the upper aero-digestive tract. To date only three cases of nasal perivascular epithelioid cell neoplasms have been reported in the literature. The present report refers to a 22-year old woman, without any stigmata of tuberous sclerosis complex, with early onset of a polypoid nasal mass with pathological and immunohistochemical features entirely compatible with those of a perivascular epithelioid cell neoplasm.

Original languageItalian
Pages (from-to)198-201
Number of pages4
JournalActa Otorhinolaryngologica Italica
Volume32
Issue number3
Publication statusPublished - Jun 2012

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ASJC Scopus subject areas

  • Otorhinolaryngology

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