Echocardiographic diagnosis of totally anomalous pulmonary venous connection to the azygos vein

Anna Maria Musolino, Giuseppe Santoro, Bruno Marino, Roberto Formigari, Paolo Guccione, Luciano Pasquini

Research output: Contribution to journalArticle

Abstract

Totally anomalous pulmonary venous connection to the azygos vein is a rare congenital heart malformation in which all the pulmonary venous blood returns anomalously to the azygos vein. Among 111 consecutive patients with totally anomalous pulmonary venous connection undergoing surgical correction at our institution between June 1982 and September 1997, this malformation was present in seven cases. By echocardiography, using a subxyphoid short-axis view at the atrial level and a modified suprasternal sagittal view, the malformation was diagnosed when the pulmonary venous confluence was traced posteriorly and superiorly relative to the right pulmonary artery and right bronchus, finally reaching reach the superior caval vein. Totally anomalous pulmonary venous connection to the azygos vein was misdiagnosed in the first two patients, both by echocardiography and angiocardiography. In the subsequent five patients, a precise diagnosis was obtained by echocardiography. Echocardiography, therefore, can be considered an accurate diagnostic tool permitting recognition of totally anomalous pulmonary venous connection to the azygos vein, and permitting corrective surgery without recourse to catheterization and angiography.

Original languageEnglish
Pages (from-to)305-309
Number of pages5
JournalCardiology in the Young
Volume9
Issue number3
Publication statusPublished - 1999

Keywords

  • Echocardiography
  • Totally anomalous pulmonary venous connection

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pediatrics, Perinatology, and Child Health

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    Musolino, A. M., Santoro, G., Marino, B., Formigari, R., Guccione, P., & Pasquini, L. (1999). Echocardiographic diagnosis of totally anomalous pulmonary venous connection to the azygos vein. Cardiology in the Young, 9(3), 305-309.