Electromyographic examination and studies of motor and sensory conduction velocities were performed in 11 patients with a presumptive diagnosis of olivopontocerebellar atrophy with autosomal dominant transmission. Peripheral nervous system involvement was shown in eight. In two patients with early onset of disease, electrophysiological alterations clearly pointed to severe axonal degeneration, whereas in six they were compatible with slight demyelination.
- Axonal degeneration
- Motor and sensory conduction velocities
- Olivopontocerebellar atrophy
ASJC Scopus subject areas
- Clinical Neurology