Erdheim-Chester disease: imaging-guided therapeutic approach.

Emanuel Della Torre, Lorenzo Dagna, Paola Mapelli, Renata Mellone, Maria Grazia Sabbadini

Research output: Contribution to journalArticle

Abstract

Erdheim-Chester disease (ECD) is a rare form of systemic non-Langerhans cell histiocytosis with characteristic bone involvement. However, extraskeletal involvement occurs in approximately half of the patients. Because of its protean findings, the diagnosis of ECD is often delayed; thus, a clinical suspicion may prompt specific imaging studies to recognize suggestive signs of organ involvement. In this study, a case of a patient with ECD with representative progressive multisystemic involvement has been reported; although the final diagnosis was confirmed by histologic analysis, imaging studies with almost pathognomonic findings guided the diagnostic process and prompted different therapeutic approaches according to the localization of the disease.

Original languageEnglish
Pages (from-to)704-706
Number of pages3
JournalClinical Nuclear Medicine
Volume36
Issue number8
Publication statusPublished - Aug 2011

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

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  • Cite this

    Della Torre, E., Dagna, L., Mapelli, P., Mellone, R., & Grazia Sabbadini, M. (2011). Erdheim-Chester disease: imaging-guided therapeutic approach. Clinical Nuclear Medicine, 36(8), 704-706.