Valutazione di una nuova miscela di aminoacidi per il trattamento della fenilchetonuria

R. Cerone; C. Barella; A. R. Fantasia; M. C. Schiaffino

Valutazione di una nuova miscela di aminoacidi per il trattamento della fenilchetonuria

Translated title of the contribution: Evaluation of a new aminoacid mixture for treatment of phenylketonuria

R. Cerone, C. Barella, A. R. Fantasia, M. C. Schiaffino

Istituto "Giannina Gaslini"

Research output: Contribution to journal › Article › peer-review

Abstract

Background. To assess the acceptability and nutritional adequacy of a new phenylalanine-free amino acid mixture (Phenylade-Dietetic Metabolic Food). Methods. Twenty PKU patients (aged 2.6-10 years) diagnosed and followed by our Department. The children were given this product for a minimum of 4 and a maximum of 12 months. The clinical control has been carried out before treatment and then every 3 months. The biochemical parameters included: quantitative plasma amino acids, hematologic measurements of nutritional adequacy folic acid and vitamin B₁₂. Results. All patients (except one) found this new product to be an acceptable alternatives as to taste and convenience to the previous low phenylalanine protein substitutes. Conclusions. Normal growth was maintained.

Translated title of the contribution	Evaluation of a new aminoacid mixture for treatment of phenylketonuria
Original language	Italian
Pages (from-to)	403-406
Number of pages	4
Journal	Minerva Pediatrica
Volume	51
Issue number	11-12
Publication status	Published - Nov 1999

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health

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title = "Valutazione di una nuova miscela di aminoacidi per il trattamento della fenilchetonuria",

abstract = "Background. To assess the acceptability and nutritional adequacy of a new phenylalanine-free amino acid mixture (Phenylade-Dietetic Metabolic Food). Methods. Twenty PKU patients (aged 2.6-10 years) diagnosed and followed by our Department. The children were given this product for a minimum of 4 and a maximum of 12 months. The clinical control has been carried out before treatment and then every 3 months. The biochemical parameters included: quantitative plasma amino acids, hematologic measurements of nutritional adequacy folic acid and vitamin B12. Results. All patients (except one) found this new product to be an acceptable alternatives as to taste and convenience to the previous low phenylalanine protein substitutes. Conclusions. Normal growth was maintained.",

keywords = "Amino acids pharmacology, Phenylalanine metabolism, Phenylketonuria, diet therapy",

author = "R. Cerone and C. Barella and Fantasia, {A. R.} and Schiaffino, {M. C.}",

year = "1999",

month = nov,

language = "Italian",

volume = "51",

pages = "403--406",

journal = "Minerva Pediatrica",

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publisher = "Edizioni Minerva Medica S.p.A.",

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TY - JOUR

T1 - Valutazione di una nuova miscela di aminoacidi per il trattamento della fenilchetonuria

AU - Cerone, R.

AU - Barella, C.

AU - Fantasia, A. R.

AU - Schiaffino, M. C.

PY - 1999/11

Y1 - 1999/11

N2 - Background. To assess the acceptability and nutritional adequacy of a new phenylalanine-free amino acid mixture (Phenylade-Dietetic Metabolic Food). Methods. Twenty PKU patients (aged 2.6-10 years) diagnosed and followed by our Department. The children were given this product for a minimum of 4 and a maximum of 12 months. The clinical control has been carried out before treatment and then every 3 months. The biochemical parameters included: quantitative plasma amino acids, hematologic measurements of nutritional adequacy folic acid and vitamin B12. Results. All patients (except one) found this new product to be an acceptable alternatives as to taste and convenience to the previous low phenylalanine protein substitutes. Conclusions. Normal growth was maintained.

AB - Background. To assess the acceptability and nutritional adequacy of a new phenylalanine-free amino acid mixture (Phenylade-Dietetic Metabolic Food). Methods. Twenty PKU patients (aged 2.6-10 years) diagnosed and followed by our Department. The children were given this product for a minimum of 4 and a maximum of 12 months. The clinical control has been carried out before treatment and then every 3 months. The biochemical parameters included: quantitative plasma amino acids, hematologic measurements of nutritional adequacy folic acid and vitamin B12. Results. All patients (except one) found this new product to be an acceptable alternatives as to taste and convenience to the previous low phenylalanine protein substitutes. Conclusions. Normal growth was maintained.

KW - Amino acids pharmacology

KW - Phenylalanine metabolism

KW - Phenylketonuria, diet therapy

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