Eyelid myoclonia with absences (Jeavons syndrome): A well-defined idiopathic generalized epilepsy syndrome or a spectrum of photosensitive conditions?

Salvatore Striano, Giuseppe Capovilla, Vito Sofia, Antonino Romeo, Guido Rubboli, Pasquale Striano, Dorothée Kasteleijn Nolst Trenité

Research output: Contribution to journalArticle

Abstract

Eyelid myoclonia with absences (EMA), or Jeavons syndrome, is a generalized epileptic condition clinically characterized by eyelid myoclonia (EM) with or without absences, eye closure-induced electroencephalography (EEG) paroxysms, and photosensitivity; in addition, rare tonic-clonic seizures may also occur. Although first described in 1977 and widely reported by several authors within the last few years, EMA has not been yet recognized as a definite epileptic syndrome. However, when strict criteria are applied to the diagnosis, EMA appears to be a distinctive condition that could be considered a myoclonic epileptic syndrome, with myoclonia limited to the eyelids, rather than an epileptic syndrome with absences.

Original languageEnglish
Pages (from-to)15-19
Number of pages5
JournalEpilepsia
Volume50
Issue numberSUPPL. 5
DOIs
Publication statusPublished - May 2009

Keywords

  • Epilepsy
  • Eyelid myoclonia
  • Eyelid myoclonia with absences
  • Myoclonus
  • Photosensitivity

ASJC Scopus subject areas

  • Clinical Neurology
  • Neurology

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