Fahr's disease presenting with dementia at onset: A case report and literature review

Research output: Contribution to journalArticlepeer-review

Abstract

Fahr's disease (FD) is characterized by sporadic or familiar idiopathic calcification of the basal ganglia, dentate nuclei of the cerebellum, and centrum semiovale, mainly presenting with movement disorder, dementia, and behavioral abnormalities. We described a rare case of Fahr's disease presenting at onset only with behavioral and neuropsychological alterations, whose diagnosis was supposed only after a brain CT, which showed extensive bilateral calcifications in the dentate nuclei of the cerebellum and basal ganglia. Since the onset of Fahr's disease may be a dysexecutive syndrome with behavioral abnormalities, the clinical and radiological features are really important to do the appropriate diagnosis.

Original languageEnglish
Article number750975
JournalBehavioural Neurology
Volume2014
DOIs
Publication statusPublished - 2014

ASJC Scopus subject areas

  • Neuropsychology and Physiological Psychology
  • Clinical Neurology
  • Neurology
  • Medicine(all)

Fingerprint Dive into the research topics of 'Fahr's disease presenting with dementia at onset: A case report and literature review'. Together they form a unique fingerprint.

Cite this