TY - JOUR
T1 - Fahr's disease presenting with dementia at onset
T2 - A case report and literature review
AU - CalabrÒ, Rocco Salvatore
AU - Spadaro, Letteria
AU - Marra, Angela
AU - Bramanti, Placido
PY - 2014
Y1 - 2014
N2 - Fahr's disease (FD) is characterized by sporadic or familiar idiopathic calcification of the basal ganglia, dentate nuclei of the cerebellum, and centrum semiovale, mainly presenting with movement disorder, dementia, and behavioral abnormalities. We described a rare case of Fahr's disease presenting at onset only with behavioral and neuropsychological alterations, whose diagnosis was supposed only after a brain CT, which showed extensive bilateral calcifications in the dentate nuclei of the cerebellum and basal ganglia. Since the onset of Fahr's disease may be a dysexecutive syndrome with behavioral abnormalities, the clinical and radiological features are really important to do the appropriate diagnosis.
AB - Fahr's disease (FD) is characterized by sporadic or familiar idiopathic calcification of the basal ganglia, dentate nuclei of the cerebellum, and centrum semiovale, mainly presenting with movement disorder, dementia, and behavioral abnormalities. We described a rare case of Fahr's disease presenting at onset only with behavioral and neuropsychological alterations, whose diagnosis was supposed only after a brain CT, which showed extensive bilateral calcifications in the dentate nuclei of the cerebellum and basal ganglia. Since the onset of Fahr's disease may be a dysexecutive syndrome with behavioral abnormalities, the clinical and radiological features are really important to do the appropriate diagnosis.
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U2 - 10.1155/2014/750975
DO - 10.1155/2014/750975
M3 - Article
C2 - 24803731
AN - SCOPUS:84898637556
VL - 2014
JO - Behavioural Neurology
JF - Behavioural Neurology
SN - 0953-4180
M1 - 750975
ER -