We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution.
|Number of pages||5|
|Publication status||Published - Nov 1987|
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health