Fibrous dysplasia of the orbital region: Current clinical perspectives in ophthalmology and cranio-maxillofacial surgery

Mario Goisis, Federico Biglioli, Magda Guareschi, Alice Frigerio, Pietro Mortini

Research output: Contribution to journalArticle

27 Citations (Scopus)

Abstract

PURPOSE: To describe the multidisciplinary diagnosis and treatment of patients with orbital fibrous dysplasia, a slowly progressive disease that may lead to asymmetry, disfigurement, and functional ocular problems. METHODS: Ten patients with orbital fibrous dysplasia underwent bifrontal craniotomy through a coronal flap, with the removal of the supraorbital arch and dysplastic process involving the anterior and middle base of the skull. Four patients underwent superior orbital fissure and optic nerve canal decompression. Reconstruction was performed by using an autologous bone graft for both the adults and children, in whom a rib graft was preferred. The mean follow-up was 53.2 ± 18.3 months (range, 14 to 94 months). The patients' preoperative status and postoperative status were compared. RESULTS: The immediate and long-term morphologic and aesthetic results were good in all cases. All of the patients complained of some degree of diplopia during the immediate postoperative period, but the problem spontaneously resolved within 1 to 6 months in all but one case. No postoperative reduction in visual function was observed in the patients who underwent optic nerve decompression. The only reported complication was the irregular reabsorption of regrafted dysplastic bone in one patient. CONCLUSIONS: A multidisciplinary approach to orbital fibrous dysplasia is fundamental for treatment planning and execution.

Original languageEnglish
Pages (from-to)383-387
Number of pages5
JournalOphthalmic Plastic and Reconstructive Surgery
Volume22
Issue number5
DOIs
Publication statusPublished - Sep 2006

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Oral Surgery
Ophthalmology
Optic Nerve
Decompression
Transplants
Bone and Bones
Diplopia
Craniotomy
Skull Base
Ribs
Esthetics
Postoperative Period
Therapeutics

ASJC Scopus subject areas

  • Ophthalmology
  • Surgery

Cite this

Fibrous dysplasia of the orbital region : Current clinical perspectives in ophthalmology and cranio-maxillofacial surgery. / Goisis, Mario; Biglioli, Federico; Guareschi, Magda; Frigerio, Alice; Mortini, Pietro.

In: Ophthalmic Plastic and Reconstructive Surgery, Vol. 22, No. 5, 09.2006, p. 383-387.

Research output: Contribution to journalArticle

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