Anestesia generale nella sindrome di Cohen. Descrizione di un caso clinico.

Translated title of the contribution: General anesthesia in Cohen syndrome. Report of a clinical case

F. Cavaliere, S. Cormaci, M. Cormaci, A. Alberti

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

The case of a 23 years old woman, affected by the Cohen syndrome, who underwent general anesthesia for extensive dental surgery, is reported. The Cohen syndrome is an autosomal recessive syndrome that causes mental retardation, obesity, short stature as well as oral, ocular, and limb anomalies. The problems the anesthesiologist could deal with include the capacity of the patient to cooperate; difficult intubation because of maxillary hypoplasia, micrognathia, narrow and high-arched palate, and prominent maxillary central incisors; generalized muscular hypotonia; moderate leukopenia, that could theoretically increase the risk of infection: and, finally, possible associated mitral valve prolapse or hiatus hernia. In the case reported the presence of mitral valve prolapse or hiatus hernia was ruled out echographically. The patient was premedicated with diazepam and atropine i.m.; general anesthesia was carried out by propofol-fentanyl association and myorelaxation was obtained with atracurium. Nasotracheal intubation was performed easily in spite of oral anomalies so that the usefulness of thyromental distance, which was 7 cm long, as a clinical test to evaluate a potentially difficult intubation was confirmed. Noteworthy, the thyromental distance was the only test which was suitable for the uncooperative patient. At the end of surgery muscular tone recovered promptly and the endotracheal tube could be regularly removed. No complication was registered postoperatively.

Original languageItalian
Pages (from-to)163-166
Number of pages4
JournalMinerva Anestesiologica
Volume61
Issue number4
Publication statusPublished - Apr 1995

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Intubation
General Anesthesia
Mitral Valve Prolapse
Hiatal Hernia
Micrognathism
Atracurium
Muscle Hypotonia
Palate
Leukopenia
Fentanyl
Propofol
Incisor
Diazepam
Atropine
Intellectual Disability
Tooth
Extremities
Obesity
Infection
Cohen syndrome

ASJC Scopus subject areas

  • Anesthesiology and Pain Medicine

Cite this

Anestesia generale nella sindrome di Cohen. Descrizione di un caso clinico. / Cavaliere, F.; Cormaci, S.; Cormaci, M.; Alberti, A.

In: Minerva Anestesiologica, Vol. 61, No. 4, 04.1995, p. 163-166.

Research output: Contribution to journalArticle

Cavaliere, F, Cormaci, S, Cormaci, M & Alberti, A 1995, 'Anestesia generale nella sindrome di Cohen. Descrizione di un caso clinico.', Minerva Anestesiologica, vol. 61, no. 4, pp. 163-166.
Cavaliere, F. ; Cormaci, S. ; Cormaci, M. ; Alberti, A. / Anestesia generale nella sindrome di Cohen. Descrizione di un caso clinico. In: Minerva Anestesiologica. 1995 ; Vol. 61, No. 4. pp. 163-166.
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