Giant desmoid tumors in Gardner's syndrome: A case report and review of the literature

L. Cobianchi, S. Zonta, F. Lovisetto, V. Jemos, M. Alessiani, A. Sgarella, P. Dionigi

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Desmoid tumors are very rare and occur non-sporadically as a phenotypic variant of familial adenomatous polyposis (FAP). In this syndrome, desmoid tumors are particularly aggressive and are the second cause of death. The literature reveals that the difficulty in choosing the therapeutic strategy for these tumors is due to their location and frequent habit of recurring. We report the case of a patient with Gardner's syndrome who had already undergone a prophylactic total colectomy and then presented huge desmoid masses in his abdomen. He has been treated successfully with surgery in our Center. This experience provides support to the prevailing but still debated belief that surgery is a suitable management for these tumors.

Original languageEnglish
Pages (from-to)405-408
Number of pages4
JournalChirurgia
Volume18
Issue number5
Publication statusPublished - Oct 2005

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Gardner Syndrome
Aggressive Fibromatosis
Neoplasms
Adenomatous Polyposis Coli
Colectomy
Abdomen
Habits
Cause of Death

Keywords

  • Desmoid tumors
  • Familial adenomatosis
  • Gardner syndrome

ASJC Scopus subject areas

  • Surgery

Cite this

Giant desmoid tumors in Gardner's syndrome : A case report and review of the literature. / Cobianchi, L.; Zonta, S.; Lovisetto, F.; Jemos, V.; Alessiani, M.; Sgarella, A.; Dionigi, P.

In: Chirurgia, Vol. 18, No. 5, 10.2005, p. 405-408.

Research output: Contribution to journalArticle

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