A propos du syndrome hemiconvulsion-hemiplegie-epilepsie (HHE)

Translated title of the contribution: Hemiconvulsion-hemiplegia-epilepsy syndrome (HHE)

Renzo Guerrini, Michelle Bureau, Charlotte Dravet, Pierre Genton

Research output: Contribution to journalArticle

Abstract

The hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome has been known for a long time, but the first detailed electroclinical descriptions came from Henri Gastaut and the Marseilles school. The incidence of seizures occurring after prolonged febrile convulsions has progressively decreased over the past 30 years, due mostly to a better prevention of longlasting febrile seizures or status and to the widespread use of benzodiazepines since the 1960s; recently diagnosed cases are mostly of a symptomatic nature, and are associated with underlying brain lesions. The classical HHE syndrome is characterized by the succession of lateralized febrile seizures, focal cerebral edema and resulting various forms of focal atrophy, including hippocampal sclerosis but also other localizations and more diffuse epileptogenic lesions. Epilepsy begins between 1 and 20 years after the initial event, and seizures are not always of the typical, psychomotor type. Preventive treatment of longlasting febrile seizures is important, but there is no standard therapy for epilepsy in HHE syndrome, as many different clinical situations may be encountered in this context.

Translated title of the contributionHemiconvulsion-hemiplegia-epilepsy syndrome (HHE)
Original languageFrench
Pages (from-to)159-166
Number of pages8
JournalEpilepsies
Volume8
Issue number2
Publication statusPublished - Jun 1996

ASJC Scopus subject areas

  • Clinical Neurology

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  • Cite this

    Guerrini, R., Bureau, M., Dravet, C., & Genton, P. (1996). A propos du syndrome hemiconvulsion-hemiplegie-epilepsie (HHE). Epilepsies, 8(2), 159-166.