Studio video-poligrafico nella sindrome delle assenze con mioclonie periorali

Translated title of the contribution: Ictal video-polygraphic features of perioral myoclonia with absences

M. Trivisano, G. D'Orsi, M. G. Pascarella, E. Carapelle, R. Grasso, V. Demaio, L. M. Specchio

Research output: Contribution to journalArticlepeer-review

Abstract

There have been few case reports of perioral myoclonia with absences (POMA) because of the lack of videopolygraphic recordings clarifying the electroencephalogram (EEG)-electromyogram (EMG) correlations. We describe one of the first video-polygraphic studies of POMA in a patient who underwent repeated and prolonged split-screen video-polygraphic recordings. The ictal EEG showed generalized and irregular discharges of spikes or multiple spikes and slow waves, while two concomitant EMG patterns appeared: (1) a rhythmic enhancement of the orbicularis oris and masseter muscles on both sides with minimal asymmetry corresponding to perioral movements, and (2) a progressive increase in muscular tone in the mylohyoideus muscle corresponding to oro-alimentary automatisms. Myoclonic jerks were inconstantly time-locked to the spike component of the spike-wave complex. The evidence of a complex pattern of activation of the facial muscles suggests that the involvement of subcortical central pattern generators, related to masticatory activity, through the disinhibitory effect of the spike-wave discharge is a possible pathophysiological mechanism underlying POMA.

Translated title of the contributionIctal video-polygraphic features of perioral myoclonia with absences
Original languageItalian
Pages (from-to)122-124
Number of pages3
JournalBollettino - Lega Italiana contro l'Epilessia
Issue number144
Publication statusPublished - May 2012

ASJC Scopus subject areas

  • Clinical Neurology

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