Idiopathic myocardial vasculitis presenting as restrictive cardiomyopathy

Andrea Frustaci, Cristina Chimenti, Maurizio Pieroni

Research output: Contribution to journalArticlepeer-review

Abstract

A previously unreported case of small-vessel myocardial vasculitis presenting as restrictive cardiomyopathy and congestive heart failure is described. The hemodynamic study, showing severely increased and equalized diastolic pressures in atrial and ventricular chambers, and cardiac MRI, showing normal pericardium and ventricular endomyocardial biopsy, not including myocardial vascular component, were insufficient to make a diagnosis. This made throracotomy and surgical cardiac biopsy necessary. Steroids and cyclophosphamide, introduced after histologic evidence of necrotizing vasculitis, unassociated with a systemic disease, became available and improved the clinical profile and the diastolic dysfunction at two-dimensional echocardiographic Doppler analysis.

Original languageEnglish
Pages (from-to)1462-1464
Number of pages3
JournalChest
Volume111
Issue number5
Publication statusPublished - 1997

Keywords

  • heart failure
  • myocardial vasculitis
  • restricted cardiomyopathy

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

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