Idiopathic restrictive cardiomyopathy in childhood

M. P. Calabrò, G. Oreto, G. Vita, P. Gitto, A. Toscano, S. Consolo, G. Tortorella, I. Barberi

Research output: Contribution to journalArticlepeer-review

Abstract

We describe the clinical features of 2 female pediatric patients with idiopathic restrictive cardiomyopathy (IRCM), an uncommon disease in childhood. Patient I was diagnosed early because the symptoms of pulmonary venous congestion manifested at 14 months of age, and had a short-term unfavorable outcome. In contrast, patient 2, who suffered from skeletal myopathy, was diagnosed as having IRCM at 8 years of age; despite a severe cardiac involvement documented by ECG and echocardiogram, this patient has no cardiac symptoms at the age of 16. This study confirms that IRCM has a malignant outcome in children whenever the clinical manifestations of pulmonary congestion occur early, whereas absence of symptoms is associated with a better survival.

Original languageEnglish
Pages (from-to)412-415
Number of pages4
JournalItalian Journal of Pediatrics
Volume28
Issue number5
Publication statusPublished - Oct 2002

Keywords

  • Cardiomyopathy
  • Congestive heart failure
  • Echocardiography

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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