The Great Arteries Transposition corrected by Mustard's repair is often complicated with inferior vena cava obstruction with consequent intestinal lymphangiectasia and protein-losing enteropathy. We report a case of a 9 years old boy who underwent Mustard's repair and presented diarrhoea, abdominal pain, hypoproteinemia and ascites. The fecal elimination of 51Cr-labeled albumin was remarkable increased and the intestinal biopsy showed a noteworthy lymphangiectasia due to an hemodynamic overload. Therefore subjects with Great Arteries Transposition corrected by Mustard's repair should be valued in the post-surgical follow-up by 51Cr-labeled albumin fecal elimination and by intestinal biopsy, already sensitive in asymptomatic phase.
|Translated title of the contribution||Intestinal lymphangiectasis: late complication of transportation of the great vessels corrected by the Mustard technic. A clinical case|
|Number of pages||3|
|Journal||Pediatria Medica e Chirurgica|
|Publication status||Published - Sep 1982|
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health