Abstract
Objective. Eosinophilic fasciitis is an uncommon scleroderma-like disorder characterised by induration and thickening of skin and soft tissue, usually associated with peripheral eosinophilia, poorly characterised in childhood. Methods. We report 3 paediatric cases of eosinophilic fasciitis showing unusual clinical and histopathological features with a review of the literature. Results. All cases presented progressive motility impairment started from upper limbs with no skin abnormalities. All cases showed systemic inflammatory involvement and 2 patients had acute complications. Two patients developed disabling outcomes despite appropriate treatments. Conclusion. Eosinophilic fasciitis may present unusual clinical and histopathological features during childhood and requires early recognition in order to prevent acute complications and disabling outcomes.
| Original language | English |
|---|---|
| Pages (from-to) | 527-530 |
| Number of pages | 4 |
| Journal | Clinical and Experimental Rheumatology |
| Volume | 34 |
| Issue number | 3 |
| Publication status | Published - 2016 |
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Keywords
- Eosinophilia
- Juvenile-onset scleroderma
- Paediatrics
- Rheumatology
ASJC Scopus subject areas
- Medicine(all)
Cite this
Juvenile eosinophilic fasciitis : Three case reports with a review of the literature. / Papa, Riccardo; Nozza, Paolo; Granata, Claudio; Caorsi, Roberta; Gattorno, Marco; Martini, Alberto; Picco, Paolo.
In: Clinical and Experimental Rheumatology, Vol. 34, No. 3, 2016, p. 527-530.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Juvenile eosinophilic fasciitis
T2 - Three case reports with a review of the literature
AU - Papa, Riccardo
AU - Nozza, Paolo
AU - Granata, Claudio
AU - Caorsi, Roberta
AU - Gattorno, Marco
AU - Martini, Alberto
AU - Picco, Paolo
PY - 2016
Y1 - 2016
N2 - Objective. Eosinophilic fasciitis is an uncommon scleroderma-like disorder characterised by induration and thickening of skin and soft tissue, usually associated with peripheral eosinophilia, poorly characterised in childhood. Methods. We report 3 paediatric cases of eosinophilic fasciitis showing unusual clinical and histopathological features with a review of the literature. Results. All cases presented progressive motility impairment started from upper limbs with no skin abnormalities. All cases showed systemic inflammatory involvement and 2 patients had acute complications. Two patients developed disabling outcomes despite appropriate treatments. Conclusion. Eosinophilic fasciitis may present unusual clinical and histopathological features during childhood and requires early recognition in order to prevent acute complications and disabling outcomes.
AB - Objective. Eosinophilic fasciitis is an uncommon scleroderma-like disorder characterised by induration and thickening of skin and soft tissue, usually associated with peripheral eosinophilia, poorly characterised in childhood. Methods. We report 3 paediatric cases of eosinophilic fasciitis showing unusual clinical and histopathological features with a review of the literature. Results. All cases presented progressive motility impairment started from upper limbs with no skin abnormalities. All cases showed systemic inflammatory involvement and 2 patients had acute complications. Two patients developed disabling outcomes despite appropriate treatments. Conclusion. Eosinophilic fasciitis may present unusual clinical and histopathological features during childhood and requires early recognition in order to prevent acute complications and disabling outcomes.
KW - Eosinophilia
KW - Juvenile-onset scleroderma
KW - Paediatrics
KW - Rheumatology
UR - http://www.scopus.com/inward/record.url?scp=84982862087&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84982862087&partnerID=8YFLogxK
M3 - Article
C2 - 27268780
AN - SCOPUS:84982862087
VL - 34
SP - 527
EP - 530
JO - Clinical and Experimental Rheumatology
JF - Clinical and Experimental Rheumatology
SN - 0392-856X
IS - 3
ER -