Left renal vein leiomyosarcoma

Leiomyosarcomas are rare but malignant tumors; 60% of them are localized in inferior vein cava district. We present the case report of a 33-year-old man with left renal vein leiomyosarcoma presenting with hematuria and back pain; a computed tomography scan showed a solid mass in left renal pelvis with a diameter of 49x47 mm, with central necrotica areas and esofitic development directed to pelvis; no sign of dilatation of the collecting system. We made a total right nefrectomy removing the tumor, perirenal fat tissue, homolateral adrenal gland and paraortic and renal hilum linfonodes. The tumor was solid, white, with hard-elastic thickness and maximum diameter of 5 cm, close to the hilum. Definitive diagnosis of vascular wall leiomyosarcoma has been reached thanks to the anatomopathological results; neither kidney nor other structures were involved by the mass; all nodes were negatives. At moment the patient is in good clinical conditions.