Lymphoproliferative disease and acquired C1 inhibitor deficiency

Roberto Castelli, Daniela Lambertenghi Deliliers, Lorenza C. Zingale, Enrico Maria Pogliani, Marco Cicardi

Research output: Contribution to journalArticle

48 Citations (Scopus)

Abstract

Angioedema due to acquired deficiency of the C1-inhibitor is a bridging condition between autoimmunity and lymphoproliferation. We report 32 patients with acquired C1 inhibitor deficiency: 23 have anti C1-inhibitor autoantibodies; 13 have monoclonal gammopathies of unknown significance and 9 have non-Hodgkin's lymphoma. Our series suggest that different forms of B cell disorders coexist and/or evolve into each other in acquired angioedema.

Original languageEnglish
Pages (from-to)716-718
Number of pages3
JournalHaematologica
Volume92
Issue number5
DOIs
Publication statusPublished - May 2007

Fingerprint

Hereditary Angioedemas
Angioedema
Paraproteinemias
Autoimmunity
Autoantibodies
Non-Hodgkin's Lymphoma
B-Lymphocytes
Acquired angioedema

Keywords

  • Acquired
  • Autoantibody
  • C1 inhibitor
  • Deficiency
  • Lymphoproliferative

ASJC Scopus subject areas

  • Hematology

Cite this

Castelli, R., Deliliers, D. L., Zingale, L. C., Pogliani, E. M., & Cicardi, M. (2007). Lymphoproliferative disease and acquired C1 inhibitor deficiency. Haematologica, 92(5), 716-718. https://doi.org/10.3324/haematol.10769

Lymphoproliferative disease and acquired C1 inhibitor deficiency. / Castelli, Roberto; Deliliers, Daniela Lambertenghi; Zingale, Lorenza C.; Pogliani, Enrico Maria; Cicardi, Marco.

In: Haematologica, Vol. 92, No. 5, 05.2007, p. 716-718.

Research output: Contribution to journalArticle

Castelli, R, Deliliers, DL, Zingale, LC, Pogliani, EM & Cicardi, M 2007, 'Lymphoproliferative disease and acquired C1 inhibitor deficiency', Haematologica, vol. 92, no. 5, pp. 716-718. https://doi.org/10.3324/haematol.10769
Castelli R, Deliliers DL, Zingale LC, Pogliani EM, Cicardi M. Lymphoproliferative disease and acquired C1 inhibitor deficiency. Haematologica. 2007 May;92(5):716-718. https://doi.org/10.3324/haematol.10769
Castelli, Roberto ; Deliliers, Daniela Lambertenghi ; Zingale, Lorenza C. ; Pogliani, Enrico Maria ; Cicardi, Marco. / Lymphoproliferative disease and acquired C1 inhibitor deficiency. In: Haematologica. 2007 ; Vol. 92, No. 5. pp. 716-718.
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