Lymphoproliferative disease and acquired C1 inhibitor deficiency

Roberto Castelli, Daniela Lambertenghi Deliliers, Lorenza C. Zingale, Enrico Maria Pogliani, Marco Cicardi

Research output: Contribution to journalArticlepeer-review


Angioedema due to acquired deficiency of the C1-inhibitor is a bridging condition between autoimmunity and lymphoproliferation. We report 32 patients with acquired C1 inhibitor deficiency: 23 have anti C1-inhibitor autoantibodies; 13 have monoclonal gammopathies of unknown significance and 9 have non-Hodgkin's lymphoma. Our series suggest that different forms of B cell disorders coexist and/or evolve into each other in acquired angioedema.

Original languageEnglish
Pages (from-to)716-718
Number of pages3
Issue number5
Publication statusPublished - May 2007


  • Acquired
  • Autoantibody
  • C1 inhibitor
  • Deficiency
  • Lymphoproliferative

ASJC Scopus subject areas

  • Hematology


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