Main genetic entities associated with supernumerary teeth

Francisco Cammarata-Scalisi, Andrea Avendaño, Michele Callea

Research output: Contribution to journalArticlepeer-review


Supernumerary teeth represent a common human dental anomaly, defined as presence of extra teeth-more than the normal number foreseen in primary or permanent dentition. The prevalence has been reported between 0.2 to 3%, and is more frequent in males than females. The etiology is heterogeneous, highly variable and most of the cases are idiopathic. However, the presence of multiple impacted or erupted supernumerary teeth is rare and associated with some genetic syndromes: cleidocranial displasia, familial adenomatous polyposis, trichorhinophalangeal syndrome type I, Rubinstein-Taybi syndrome, Nance-Horan syndrome, Opitz G/BBB syndrome, oculofaciocardiodental syndrome and Robinow syndrome (autosomal dominant). The supernumerary teeth should be considered in order to possibly diagnose these entities with the aim of offering an interdisciplinary management and treatment, as well as offer adequate family genetic counseling.

Original languageEnglish
Pages (from-to)437-444
Number of pages7
JournalArchivos Argentinos de Pediatria
Issue number6
Publication statusPublished - Dec 1 2018


Dive into the research topics of 'Main genetic entities associated with supernumerary teeth'. Together they form a unique fingerprint.

Cite this