Marfan's syndrome, recurrent complex partial status epilepticus and myoclonus: A case report

G. Ambrosetto, P. Tinuper, C. A. Tassinari

Research output: Contribution to journalArticle

Abstract

A 26-year-old mentally retarded woman suffering from Marfan's syndrome and epileptic seizures presented weekly recurrent complex partial status epilepticus for two years, and myoclonus at rest. A marked increase of the myoclonic jerks and transient signs of cerebellar dysfunction followed each occurrence of the status epilepticus. Myoclonus could be interpreted as: 1) a permanent neurologic consequence of primary CNS disorders or secondary to disorders of the connective tissue, 2) a persistent post-ictal sequela sustained by recurrence of complex partial status, or 3) an additional consequence of both brain disorders due to Marfan's syndrome and recurrence of complex partial status epilepticus. The case report raises the possibility that recurrence of complex partial status for a long period may be a risk factor of permanent neurologic deficit, especially in already brain damaged patients.

Original languageEnglish
Pages (from-to)33-36
Number of pages4
JournalClinical EEG Electroencephalography
Volume19
Issue number1
Publication statusPublished - 1988

ASJC Scopus subject areas

  • Clinical Neurology

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