Memory abilities in children with Williams syndrome

Stefano Vicari, Daniela Brizzolara, Giovanni Augusto Carlesimo, Grazia Pezzini, Virginia Volterra

Research output: Contribution to journalArticle

Abstract

Williams syndrome (WS) is a rare genetic condition characterised by intellectual disability, typical facial dysmorphology and several medical anomalies. A specific neuropsychological profile with a dissociation between language (relatively preserved) and visuo-spatial abilities (more seriously impaired) has been hypothesised in these children. Memory abilities of these patients have not been adequately investigated, although they may substantially contribute to better understanding their neuropsychological profile. The present study aimed at investigating verbal and spatial memory in patients with WS (N = 16). Their performance was compared with that of normally developing children on tasks of verbal and spatial span and immediate and delayed recall of verbal and visuoperceptual materials. Memory abilities of WS children appear to be characterised by defective visuo-spatial memory, both in the short-term and long-term domain, and a dissociation between normal short- but deficient long-term verbal learning. Results are interpreted by supporting the thesis that intellectual disability reflects the defective functioning of a complex system in which some cognitive competencies may be disrupted more than others.

Original languageEnglish
Pages (from-to)503-514
Number of pages12
JournalCortex
Volume32
Issue number3
Publication statusPublished - 1996

Fingerprint

Williams Syndrome
Aptitude
Intellectual Disability
Verbal Learning
Short-Term Memory
Language
Spatial Memory

ASJC Scopus subject areas

  • Experimental and Cognitive Psychology
  • Neuropsychology and Physiological Psychology
  • Cognitive Neuroscience
  • Neuroscience(all)

Cite this

Vicari, S., Brizzolara, D., Carlesimo, G. A., Pezzini, G., & Volterra, V. (1996). Memory abilities in children with Williams syndrome. Cortex, 32(3), 503-514.

Memory abilities in children with Williams syndrome. / Vicari, Stefano; Brizzolara, Daniela; Carlesimo, Giovanni Augusto; Pezzini, Grazia; Volterra, Virginia.

In: Cortex, Vol. 32, No. 3, 1996, p. 503-514.

Research output: Contribution to journalArticle

Vicari, S, Brizzolara, D, Carlesimo, GA, Pezzini, G & Volterra, V 1996, 'Memory abilities in children with Williams syndrome', Cortex, vol. 32, no. 3, pp. 503-514.
Vicari S, Brizzolara D, Carlesimo GA, Pezzini G, Volterra V. Memory abilities in children with Williams syndrome. Cortex. 1996;32(3):503-514.
Vicari, Stefano ; Brizzolara, Daniela ; Carlesimo, Giovanni Augusto ; Pezzini, Grazia ; Volterra, Virginia. / Memory abilities in children with Williams syndrome. In: Cortex. 1996 ; Vol. 32, No. 3. pp. 503-514.
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